| E80 | Disorders of porphyrin and bilirubin metabolism |
| E80.0 | Hereditary erythropoietic porphyria |
| E80.1 | Porphyria cutanea tarda |
| E80.2 | Other and unspecified porphyria |
| E80.20 | Unspecified porphyria |
| E80.21 | Acute intermittent (hepatic) porphyria |
| E80.29 | Other porphyria |
| E80.3 | Defects of catalase and peroxidase |
| E80.4 | Gilbert syndrome |
| E80.5 | Crigler-Najjar syndrome |
| E80.6 | Other disorders of bilirubin metabolism |
| E80.7 | Disorder of bilirubin metabolism, unspecified |
| E83 | Disorders of mineral metabolism |
| E83.0 | Disorders of copper metabolism |
| E83.00 | Disorder of copper metabolism, unspecified |
| E83.01 | Wilson's disease |
| E83.09 | Other disorders of copper metabolism |
| E83.1 | Disorders of iron metabolism |
| E83.10 | Disorder of iron metabolism, unspecified |
| E83.11 | Hemochromatosis |
| E83.110 | Hereditary hemochromatosis |
| E83.111 | Hemochromatosis due to repeated red blood cell transfusions |
| E83.118 | Other hemochromatosis |
| E83.119 | Hemochromatosis, unspecified |
| E83.19 | Other disorders of iron metabolism |
| E83.2 | Disorders of zinc metabolism |
| E83.3 | Disorders of phosphorus metabolism and phosphatases |
| E83.30 | Disorder of phosphorus metabolism, unspecified |
| E83.31 | Familial hypophosphatemia |
| E83.32 | Hereditary vitamin D-dependent rickets (type 1) (type 2) |
| E83.39 | Other disorders of phosphorus metabolism |
| E83.4 | Disorders of magnesium metabolism |
| E83.40 | Disorders of magnesium metabolism, unspecified |
| E83.41 | Hypermagnesemia |
| E83.42 | Hypomagnesemia |
| E83.49 | Other disorders of magnesium metabolism |
| E83.5 | Disorders of calcium metabolism |
| E83.50 | Unspecified disorder of calcium metabolism |
| E83.51 | Hypocalcemia |
| E83.52 | Hypercalcemia |
| E83.59 | Other disorders of calcium metabolism |
| E83.8 | Other disorders of mineral metabolism |
| E83.81 | Hungry bone syndrome |
| E83.89 | Other disorders of mineral metabolism |
| E83.9 | Disorder of mineral metabolism, unspecified |
| E84 | Cystic fibrosis |
| E84.0 | Cystic fibrosis with pulmonary manifestations |
| E84.1 | Cystic fibrosis with intestinal manifestations |
| E84.11 | Meconium ileus in cystic fibrosis |
| E84.19 | Cystic fibrosis with other intestinal manifestations |
| E84.8 | Cystic fibrosis with other manifestations |
| E84.9 | Cystic fibrosis, unspecified |
| E85 | Amyloidosis |
| E85.0 | Non-neuropathic heredofamilial amyloidosis |
| E85.1 | Neuropathic heredofamilial amyloidosis |
| E85.2 | Heredofamilial amyloidosis, unspecified |
| E85.3 | Secondary systemic amyloidosis |
| E85.4 | Organ-limited amyloidosis |
| E85.8 | Other amyloidosis |
| E85.81 | Light chain (AL) amyloidosis |
| E85.82 | Wild-type transthyretin-related (ATTR) amyloidosis |
| E85.89 | Other amyloidosis |
| E85.9 | Amyloidosis, unspecified |
| E86 | Volume depletion |
| E86.0 | Dehydration |
| E86.1 | Hypovolemia |
| E86.9 | Volume depletion, unspecified |
| E87 | Other disorders of fluid, electrolyte and acid-base balance |
| E87.0 | Hyperosmolality and hypernatremia |
| E87.1 | Hypo-osmolality and hyponatremia |
| E87.2 | Acidosis |
| E87.20 | Acidosis, unspecified |
| E87.21 | Acute metabolic acidosis |
| E87.22 | Chronic metabolic acidosis |
| E87.29 | Other acidosis |
| E87.3 | Alkalosis |
| E87.4 | Mixed disorder of acid-base balance |
| E87.5 | Hyperkalemia |
| E87.6 | Hypokalemia |
| E87.7 | Fluid overload |
| E87.70 | Fluid overload, unspecified |
| E87.71 | Transfusion associated circulatory overload |
| E87.79 | Other fluid overload |
| E87.8 | Other disorders of electrolyte and fluid balance, not elsewhere classified |
| E88 | Other and unspecified metabolic disorders |
| E88.0 | Disorders of plasma-protein metabolism, not elsewhere classified |
| E88.01 | Alpha-1-antitrypsin deficiency |
| E88.02 | Plasminogen deficiency |
| E88.09 | Other disorders of plasma-protein metabolism, not elsewhere classified |
| E88.1 | Lipodystrophy, not elsewhere classified |
| E88.2 | Lipomatosis, not elsewhere classified |
| E88.3 | Tumor lysis syndrome |
| E88.4 | Mitochondrial metabolism disorders |
| E88.40 | Mitochondrial metabolism disorder, unspecified |
| E88.41 | MELAS syndrome |
| E88.42 | MERRF syndrome |
| E88.49 | Other mitochondrial metabolism disorders |
| E88.8 | Other specified metabolic disorders |
| E88.81 | Metabolic syndrome |
| E88.89 | Other specified metabolic disorders |
| E88.9 | Metabolic disorder, unspecified |
| E89 | Postprocedural endocrine and metabolic complications and disorders, not elsewhere classified |
| E89.0 | Postprocedural hypothyroidism |
| E89.1 | Postprocedural hypoinsulinemia |
| E89.2 | Postprocedural hypoparathyroidism |
| E89.3 | Postprocedural hypopituitarism |
| E89.4 | Postprocedural ovarian failure |
| E89.40 | Asymptomatic postprocedural ovarian failure |
| E89.41 | Symptomatic postprocedural ovarian failure |
| E89.5 | Postprocedural testicular hypofunction |
| E89.6 | Postprocedural adrenocortical (-medullary) hypofunction |
| E89.8 | Other postprocedural endocrine and metabolic complications and disorders |
| E89.81 | Postprocedural hemorrhage of an endocrine system organ or structure following a procedure |
| E89.810 | Postprocedural hemorrhage of an endocrine system organ or structure following an endocrine system procedure |
| E89.811 | Postprocedural hemorrhage of an endocrine system organ or structure following other procedure |
| E89.82 | Postprocedural hematoma and seroma of an endocrine system organ or structure |
| E89.820 | Postprocedural hematoma of an endocrine system organ or structure following an endocrine system procedure |
| E89.821 | Postprocedural hematoma of an endocrine system organ or structure following other procedure |
| E89.822 | Postprocedural seroma of an endocrine system organ or structure following an endocrine system procedure |
| E89.823 | Postprocedural seroma of an endocrine system organ or structure following other procedure |
| E89.89 | Other postprocedural endocrine and metabolic complications and disorders |