I27.0: Primary pulmonary hypertension

Inclusion Terms

  • Heritable pulmonary arterial hypertension
  • Idiopathic pulmonary arterial hypertension
  • Primary group 1 pulmonary hypertension
  • Primary pulmonary arterial hypertension

Excludes1

  • persistent pulmonary hypertension of newborn (P29.30)
  • pulmonary hypertension NOS (I27.20)
  • secondary pulmonary arterial hypertension (I27.21)
  • secondary pulmonary hypertension (I27.29)