Q82.2: Congenital cutaneous mastocytosis
Inclusion Terms
- Congenital diffuse cutaneous mastocytosis
- Congenital maculopapular cutaneous mastocytosis
- Congenital urticaria pigmentosa
Excludes1
- cutaneous mastocytosis NOS (D47.01)
- diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
- malignant mastocytosis (C96.2-)
- systemic mastocytosis (D47.02)
- urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)