Activated Phosphoinositide 3-kinase Delta Syndrome Notes: p110d-activating mutation causing senescent T cells, lymphadenopathy, and immunodeficiency disease
D83.9 Common variable immunodeficiency, unspecified
Common variable immunodeficiency, unspecified
D86.8 Sarcoidosis of other sites Notes: Tubulo-interstitial nephropathy in sarcoidosis ; Polyarthritis in sarcoidosis ; Hepati…
Sarcoidosis of other sites Notes: Tubulo-interstitial nephropathy in sarcoidosis ; Polyarthritis in sarcoidosis ; Hepatic granuloma ; Uveoparotid fever
D81.89 Other combined immunodeficiencies
Other combined immunodeficiencies
D84 Other immunodeficiencies Notes: C1 esterase inhibitor [C1-INH] deficiency ; Immunodeficiency due to (current or past) me…
Other immunodeficiencies Notes: C1 esterase inhibitor deficiency ; Immunodeficiency due to (current or past) medication ; Immunocompromised NOS ; Immunodeficient NOS ; Immunosuppressed NOS ; code for ...
D86.81 Sarcoid meningitis
Sarcoid meningitis
D81.9 Combined immunodeficiency, unspecified Notes: Severe combined immunodeficiency disorder [SCID] NOS
Combined immunodeficiency, unspecified Notes: Severe combined immunodeficiency disorder NOS
D84.0 Lymphocyte function antigen-1 [LFA-1] defect
Lymphocyte function antigen-1 defect

