Hereditary factor IX deficiency Notes: Christmas disease ; Factor IX deficiency (with functional defect) ; Hemophilia B ; Plasma thromboplastin component deficiency
D68.3 Hemorrhagic disorder due to circulating anticoagulants Notes: Autoimmune hemophilia ; Autoimmune inhibitors to clotting …
Hemorrhagic disorder due to circulating anticoagulants Notes: Autoimmune hemophilia ; Autoimmune inhibitors to clotting factors ; Secondary hemophilia ; Lupus anticoagulant (LAC) with hemorrhagic diso ...
D68.9 Coagulation defect, unspecified
Coagulation defect, unspecified
D70 Neutropenia Notes: Congenital neutropenia ; Infantile genetic agranulocytosis ; Kostmann’s disease ; Cyclic hematopoiesi…
Neutropenia Notes: Congenital neutropenia ; Infantile genetic agranulocytosis ; Kostmann's disease ; Cyclic hematopoiesis ; Periodic neutropenia ; code for any associated: ; fever (R50.81) ; mucositis ...
D51.1 Vitamin B12 deficiency anemia due to selective vitamin B12 malabsorption with proteinuria Notes: Imerslund (Gräsbeck) sy…
Vitamin B12 deficiency anemia due to selective vitamin B12 malabsorption with proteinuria Notes: Imerslund (Gräsbeck) syndrome ; Megaloblastic hereditary anemia
D55 Anemia due to enzyme disorders Notes: Favism ; G6PD deficiency anemia ; Anemia (due to) enzyme deficiencies, except G6PD…
Anemia due to enzyme disorders Notes: Favism ; G6PD deficiency anemia ; Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate shunt pathway ; Anemia (due to) hemolytic ...
D56.8 Other thalassemias Notes: Dominant thalassemia ; Hemoglobin C thalassemia ; Mixed thalassemia ; Thalassemia with other h…
Other thalassemias Notes: Dominant thalassemia ; Hemoglobin C thalassemia ; Mixed thalassemia ; Thalassemia with other hemoglobinopathy ; hemoglobin C disease (D58.2) ; hemoglobin E disease (D58.2) ; ...
D57.218 Sickle-cell/Hb-C disease with crisis with other specified complication Notes: code to identify complications, such as: ;…
Sickle-cell/Hb-C disease with crisis with other specified complication Notes: code to identify complications, such as: ; cholelithiasis (K80.-) ; priapism (N48.32)

